Hepatic cysts of periductal gland origin presenting as obstructive jaundice

doi:10.1016/0016-5085(87)90455-0

Gastroenterology

Volume 93, Issue 4, October 1987, Pages 894-898

https://doi.org/10.1016/0016-5085(87)90455-0 Get rights and content

Abstract

Retention cysts may arise from periductal glands of the hepatic ducts. These cysts are usually asymptomatic. Presented here is the first case with jaundice secondary to obstruction of the hepatic ducts by periductal cysts. Two other cases involved asymptomatic cysts in the presence of cirrhosis, portal vein thrombosis, and hepatocellular carcinoma. This confirms the previously noted association of cysts and portal vein thrombosis. The possibility of obstruction caused by benign cysts should be considered when investigating patients with intrahepatic bile duct obstruction.

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It is a frequent condition, occurring in almost 20% of affected livers according to Terada et al. [2]. Hepatic peribiliary cysts are usually asymptomatic although very rare cases of biliary obstruction due to large perihilar cysts have been reported, causing obstructive jaundice [3]. Recently, several authors have noted that peribiliary cysts could evolve in size and number in patients with cirrhosis [4].
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It appears that only three cases (including the present case) have been reported in which a solitary small cyst (diameter < 20 mm) developed in a healthy liver and caused obstructive jaundice. Of these cases, two patients (reported in previous cases) were treated surgically, and the cysts were rated as peribiliary cysts in the postoperative pathologic examinations (13,14). The typical treatment for symptomatic liver cysts is surgery or percutaneous therapies.
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Case reportHepatic cysts of periductal gland origin presenting as obstructive jaundice

Abstract

Am J Surg

Am J Surg

Am J Surg

Proliferation of bile ducts in cirrhosis

Arch Pathol

Case report
Hepatic cysts of periductal gland origin presenting as obstructive jaundice