Main characteristics of patients with peribiliary cysts
| Characteristics | Available values | Results |
| patients | % or median (range) | |
| Age, years | 122 | 63 (4–88) |
| Males | 122 | 98/122 (80%) |
| Japanese patients | 135 | 88/135 (65%) |
| Associated conditions/diseases* | ||
| Cirrhosis (of all aetiologies) | 135 | 52/135 (38%) |
| Portal hypertension | 117 | 40/117 (34%) |
| Portal vein thrombosis | 117 | 12/117 (10%) |
| Hepatic, biliary or pancreatic neoplasms (%) | 135 | 23/135 (17%) |
| ADPKD | 135 | 15/133 (11%) |
| Liver transplantation | 135 | 5/135 (3%) |
| Primary sclerosing cholangitis | 135 | 2/135 (1.5%) |
| No associates conditions/diseases | 135 | 21/135 (15%) |
| Clinical manifestations | ||
| Asymptomatic patients | 104 | 31/104 (30%) |
| Symptomatic patients | 104 | 73/104 (70%) |
| Symptoms related to associated conditions/diseases | 73 | 38/73 (52%) |
| Symptoms related to peribiliary cyst(s) | 73 | 21/73 (29%) |
| Symptoms related to associated diseases and PBC(s) | 73 | 14/73 (19%) |
| Complications of peribilary cyst(s) | ||
| Dilated biliary tract (slight or severe) | 126 | 47/126 (36%) |
| Obstructive jaundice | 126 | 18/126 (14%) |
| Cholangitis | 104 | 13/104 (12.5%) |
| Surgical interventions | ||
| Surgical interventions | 135 | 61/133 (45%) |
| Therapeutic misadventures related to incorrect diagnosis | 61 | 20/61 (33%) |
| Follow-up | ||
| Duration of follow-up, months | 40 | 18 (1–92) |
| Increase in number and/or size of cysts | 40 | 15/40 (37.5%) |
| Mortality | ||
| Overall mortality | 122 | 29/122 (24%) |
| Death related to decompensated cirrhosis | 21 | 17/21 (81%) |
*Some patients have more than one associated disease.
ADPKD, autosomal dominant polycystic kidney disease.